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Rabbit Anti-Human ATP1A3 pAb

Rabbit Anti-Human ATP1A3 pAb

Product Number

PA9710

Alias

ATP1A3, AHC2, ATP1A1, CAPOS, DYT12, RDP

Specifications
  • 50ul
  • 100ul
Product Description
AliasATP1A3, AHC2, ATP1A1, CAPOS, DYT12, RDP
Catalog NumberPA9710
Molecular NameATP1A3
HostRabbit
Size50ul, 100ul
ClonityPolyclonal
PurificationAffinity Purification
FormulationSupply in PBS with 0.02% sodium azide, 50% glycerol, pH 7.4.
ImmunogenRecombinant fusion protein containing a sequence corresponding to a.a. 1-60 of human ATP1A3 (NP_689509.1).
ApplicationWB
Storage ConditionStore the product under sterile conditions after opening at -20℃. Avoid freeze-thaw cycles.
Shipping ConditionShipped on ice packs.
Product Declaration本产品仅用于研究用途(RUO)。不能用于诊断或直接用于人体实验。
Product Full NameRabbit Anti-Human ATP1A3 Polyclonal Antibody
FAQ
  • Q1-ATP1A3的生物学相关性是什么?

    ATP1A3是钠钾泵α3亚基,其突变导致快速发作的肌张力障碍-帕金森症(RDP)及儿童交替性偏瘫(AHC)。

  • Q2-是否适用于神经肌肉模型?

    可以,推荐使用患者来源的神经元或转基因小鼠模型,通过IHC检测ATP1A3在质膜的分布异常。

  • Q3-是否与ATP1A1或ATP1A2交叉反应?

    经测试无交叉反应,特异性针对ATP1A3。

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