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Rabbit Anti-CI072/C9orf72 Polyclonal Antibody

Rabbit Anti-CI072/C9orf72 Polyclonal Antibody

Product Number

PAV854

Alias

C9orf72-SMCR8 complex subunit, ALSFTD, DENND9, DENNL72, FTDALS, FTDALS1

Specifications
  • 100ul
Product Description
AliasC9orf72-SMCR8 complex subunit, ALSFTD, DENND9, DENNL72, FTDALS, FTDALS1
Catalog NumberPAV854
Molecular NameC9orf72 
HostRabbit
Size100ul
ClonityPolyclonal
Concentration1 mg/ml
Purificationaffinity-chromatography
Formulationsupply in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
ImmunogenThis antibody was raised against from human CI072 protein
Recommended DilutionWB 1:500-2000
Storage ConditionStore at 4℃ for for short term storage. It is recommended to aliquote to ~10ul per vial and store at -20℃ for long term storage. Avoid repeated freezing and thawing cycles.
Shipping ConditionThis product is shipped on blue ice.
Product Declaration本产品仅用于研究用途(RUO)。不能用于诊断或直接用于人体实验。
FAQ
  • Q1-C9orf72的生物学功能是什么?

    C9orf72基因六核苷酸重复扩增导致额颞叶痴呆(FTD)和肌萎缩侧索硬化症(ALS),其蛋白参与自噬及囊泡运输调控。

  • Q2-是否适用于神经退行模型?

    可以,推荐使用C9orf72重复扩增小鼠模型,通过免疫组化检测神经元内包涵体形成。

  • Q3-是否与C9orf114交叉反应?

    经测试无交叉反应,特异性针对C9orf72。

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