SMS（鞘磷脂合酶）的生物学功能是什么？

SMS催化鞘磷脂合成，其缺陷导致尼曼-匹克病（Niemann-Pick Disease）及脂质代谢紊乱。

是否适用于溶酶体贮积症研究？

可以，推荐使用患者成纤维细胞，检测鞘磷脂蓄积及溶酶体扩大。

经测试无交叉反应，特异性针对SMS。

经测试无交叉反应，特异性针对SMS。

PA16880

SMS, MRSR, SPMSY, SRS, SpS

DATASHEET MSDS

Product Description

Alias	SMS, MRSR, SPMSY, SRS, SpS
Catalog Number	PA16880
Molecular Name	SMS
Host	Rabbit
Size	50ul, 100ul
Clonity	Polyclonal
Purification	Affinity Purification
Formulation	Supply in PBS with 0.02% sodium azide, 50% glycerol, pH 7.4.
Immunogen	Recombinant fusion protein containing a sequence corresponding to a.a. 1-366 of human SMS (NP_004586.2).
Application	WB
Storage Condition	Store the product under sterile conditions after opening at -20℃. Avoid freeze-thaw cycles.
Shipping Condition	Shipped on ice packs.
Product Declaration	本产品仅用于研究用途(RUO)。不能用于诊断或直接用于人体实验。
Product Full Name	Rabbit Anti-Human SMS Polyclonal Antibody

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